Decanoylcarnitine is a decanoic acid ester of carnitine. Decanoylcarnitine bis a medium-chain acylcarnitine that may facilitate the transport of long-chain fatty acids into the mitochondria where fatty acids undergo β-oxidation. Decanoylcarnitine is used as an analytical reference standard using GC- or LC-MS methods.
Decanoylcarnitine serves as a specific diagnostic biomarker for metabolites found in medium-chain acyl-CoA dehydrogenase (MCAD) deficiency, especially in neonates, glutaric acidemia type II, celiac disease, and adolescent obesity. Secondary marker of medium-chain ketoacyl-CoA thiolase deficiency.
The product is used primarily as a control for MS/MS.
