ANTI-NIEMANN-PICK C1
- Product NameANTI-NIEMANN-PICK C1
- CAS
- CBNumberCB4751896
- MW0
- MDL NumberMFCD03455661
- MOL FileMol file
Chemical Properties
storage temp. | -20°C |
form | buffered aqueous solution |
ANTI-NIEMANN-PICK C1 Price
Product number | Packaging | Price | Product description | Buy |
---|---|---|---|---|
Sigma-Aldrich WH0004864M2 | 100μG | $209.6 | Monoclonal Anti-NPC1 antibody produced in mouse clone 4H2, purified immunoglobulin, buffered aqueous solution |
Buy |
Sigma-Aldrich HPA026618 | 100μL | $547 | Anti-NPC1 antibody produced in rabbit Prestige Antibodies? Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution |
Buy |
Sigma-Aldrich HPA026618 | 25μL | $282 | Anti-NPC1 antibody produced in rabbit Prestige Antibodies? Powered by Atlas Antibodies, affinity isolated antibody, buffered aqueous glycerol solution |
Buy |
Sigma-Aldrich SAB3500300 | 100μG | $507 | Anti-NPC1 antibody produced in rabbit affinity isolated antibody, buffered aqueous solution |
Buy |
ANTI-NIEMANN-PICK C1 Chemical Properties,Usage,Production
General Description
This gene encodes a large protein that resides in the limiting membrane of endosomes and lysosomes and mediates intracellular cholesterol trafficking via binding of cholesterol to its N-terminal domain. It is predicted to have a cytoplasmic C-terminus, 13 transmembrane domains, and 3 large loops in the lumen of the endosome - the last loop being at the N-terminus. This protein transports low-density lipoproteins to late endosomal/lysosomal compartments where they are hydrolized and released as free cholesterol. Defects in this gene cause Niemann-Pick type C disease, a rare autosomal recessive neurodegenerative disorder characterized by over accumulation of cholesterol and glycosphingolipids in late endosomal/lysosomal compartmentsPreparation Products And Raw materials
ANTI-NIEMANN-PICK C1 Suppliers
Global(10)Suppliers
Supplier | Tel | Country | ProdList | Advantage | |
---|---|---|---|---|---|
-- | CHINA | 6979 | 58 | ||
-- | sales@bioss.com.cn | CHINA | 6717 | 58 | |
-- | 1562893815@qq.com | CHINA | 6942 | 58 | |
-- | info@zzsrm.com | CHINA | 6846 | 58 | |
-- | 2090855807@qq.com | CHINA | 6063 | 58 | |
-- | xiaoshan.wu@dr-tech.com.cn | CHINA | 2839 | 58 | |
-- | beinuobio@163.com | CHINA | 6580 | 58 | |
-- | moumou@xxx.com | CHINA | 2992 | 58 | |
-- | United States | 6825 | 87 | ||
-- | United States | 3068 | 86 |
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