(3R)-3-[(E)-2-methylbut-2-enoyl]oxy-4-(trimethylazaniumyl)butanoate

Uses

Tiglylcarnitine Hydrochloride is a long-chain fatty ester of carnitine which is accumulated and released into the circulation, in fatty-acid oxidation defects. Pattern of Tiglylcarnitine Hydrochloride can be diagnostic for a number of ├Я-oxidation defects.

Definition

ChEBI: O-tiglyl-L-carnitine is an O-acyl-L-carnitine compound having trans-2-methyl-2-butenoyl (tiglyl) as the acyl substituent. It is an O-tiglylcarnitine, an O-acyl-L-carnitine, a monounsaturated fatty acyl-L-carnitine and a methyl-branched fatty acyl-L-carnitine.