D-2-HYDROXYPENTANEDIOIC ACID DISODIUM SALT
- русский язык имя
- английское имяD-2-HYDROXYPENTANEDIOIC ACID DISODIUM SALT
- CAS №103404-90-6
- CBNumberCB2266017
- ФормулаC5H9NaO5
- мольный вес172.11
- номер MDLMFCD00069573
- файл Mol103404-90-6.mol
химическое свойство
Температура плавления | >291°C (dec.) |
температура хранения | -20°C |
растворимость | PBS (pH 7.2): 10 mg/ml |
форма | A crystalline solid |
цвет | White to light yellow |
оптическая активность | [α]/D 8.5±1.5°, c = 1 in NaOH |
Растворимость в воде | Soluble to 100 mM in water |
БРН | 5318041 |
Стабильность | Hygroscopic |
ИнЧИКей | DZHFTEDSQFPDPP-HWYNEVGZSA-L |
D-2-HYDROXYPENTANEDIOIC ACID DISODIUM SALT химические свойства, назначение, производство
Описание
D-α-Hydroxyglutaric Acid (D-2-HG) is an α-hydroxy acid that is over-produced in the human neurometabolic disease D-2-hydroxyglutaric aciduria (D-2-HGA). It is normally synthesized from 2-ketoglutarate (2-KG) by hydroxyacid-oxoacid transhydrogenase (HOT), although defects in HOT are not known to be associated with D-2-HGA. Instead, type I D-2-HGA involves mutations in D-2-hydroxyglutarate dehydrogenase, which converts D-2-HG back to 2-KG. Type II D-2-HGA results from gain-of-function mutations in isocitrate dehydrogenase 2, causing it to supplement HOT in converting 2-KG to D-2-HG. In bacteria, this α-hydroxy acid may be synthesized from oxalate and propionyl-coenzyme A by an α-hydroxyglutaric acid synthetase.Химические свойства
Pale Orange SolidИспользование
A potential inhibitor of glutamate carboxypeptidase.D-2-HYDROXYPENTANEDIOIC ACID DISODIUM SALT поставщик
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