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网站主页 GAA Anti-GAA antibody-α葡萄糖苷酶/溶酶体α-葡糖苷酶抗体
  • Anti-GAA antibody-α葡萄糖苷酶/溶酶体α-葡糖苷酶抗体

Anti-GAA antibody-α葡萄糖苷酶/溶酶体α-葡糖苷酶抗体

GAA
1138 50ul 起订
1880 100ul 起订
2900 200ul 起订
上海 更新日期:2024-04-30

上海沪震实业有限公司

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联系人:陈环环
电话:021-60345367拨打
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产品详情:

中文名称:
Anti-GAA antibody-α葡萄糖苷酶/溶酶体α-葡糖苷酶抗体
英文名称:
GAA
品牌:
沪震生物
产地:
中国/上海
保存条件:
-20°C
纯度规格:
> 99%
产品类别:
抗体 一抗
抗体名:
70 kDa lysosomal alpha-glucosidase; Acid alpha glucosidase; Acid maltase; Aglucosidase alfa; Alpha glucosidase; GAA; Glucosidase alpha acid (Pompe disease glycogen storage disease type II); Glucosidase alpha acid; Glucosidase alpha; LYAG; LYAG_HUMAN; Lysosomal alpha glucosidase.
靶点:
详见说明书
宿主:
Rabbit
适应物种:
详见说明书
克隆性:
详见说明书
浓度:
1mg/ml
应用范围:
ELISA=1:5000-10000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:200-800 (石蜡切片需做抗原修复) not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.
标识物:
详见说明书
形态:
液体
亚型:
IgG
免疫原:
详见说明书
货号:
Hz-R13254
用途范围:
科研使用
规格:
50ul/100ul/200ul
是否进口:
是否单克隆:
详见说明书
保质期:
12个月
抗原来源:
详见说明书
标记物:
详见说明书
产品用途:
ELISA=1:5000-10000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:200-800 (石蜡切片需做抗原修复) not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user.

Rabbit  Anti-GAA Polyclonal Antibody
DATASHEET

Host:Rabbit

Target Protein:GAA

IR:Immunogen Range:541-640/952

Clonality:Polyclonal

Isotype:IgG

Entrez Gene:2548

Swiss Prot:P10253

Source:KLH conjugated synthetic peptide derived from human GAA/Glucosidase alpha:541-640/952 

Purification:affinity purified by Protein A

Storage:0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.

Background:This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene. [provided by RefSeq, Jul 2008].

Size:50ul

Concentration:1mg/ml

Applications:ELISA(1:5000-10000)
IHC-P(1:100-500)
IHC-F(1:100-500)
IF(1:200-800)

Cross Reactive Species:Human
Mouse
Rat
Dog
Pig
Horse
Sheep

image.png
仅供科研使用。不能用于人和动物治疗等其它临床诊断用!

GAA;70 kDa lysosomal alp;Acid alpha glucosida;Glucosidase ;Glucosidase alpha ac;Glucosidase alpha;LYAG;LYAG_HUMAN;

公司简介

上海沪震实业有限公司是一家集研发、生产和销售于一体的生命科学实验室产品生物科技企业。主营产品:试剂盒,ELISA试剂盒,抗体,重组蛋白,血清,胎牛血清,细胞,原代细胞 细胞培养试剂,常用生化试剂。

成立日期 (10年)
注册资本 100万元整
员工人数 10-50人
年营业额 ¥ 100万以内
经营模式 工厂,试剂,定制,服务
主营行业 生化试剂,细胞培养,蛋白组学,分子生物学,细胞生物学

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