3105-95-1H-HoPro-OH

产品属性：

Cas No.3105-95-1

别名 N/A

化学名 N/A

分子式 C6H11NO2

分子量 129.16

溶解度 H2O: 100 mg/mL (774.23 mM); DMSO: 1 mg/mL (7.74 mM; ultrasonic and warming and heat to 80°C)

储存条件 Store at -20°C
General tips  For obtaining a higher solubility , please warm the tube at 37 ℃ and shake it in the ultrasonic bath for a while.
Shipping Condition     Evaluation sample solution : ship with blue ice
All other available size: ship with RT , or blue ice upon request
产品描述：
H-HoPro-OH is a breakdown product of lysine, accumulates in body fluids of infants with generalized genetic peroxisomal disorders, such as Zellweger syndrome, neonatal adrenoleukodystrophy.

[1]. Mihalik SJ, et al. Peroxisomal L-pipecolic acid oxidation is deficient in liver from Zellweger syndrome patients. Pediatr Res. 1989 May;25(5):548-52.