Butyryl-L-carnitine-d3 is intended for use as an internal standard for the quantification of butyryl-L-carnitine by GC- or LC-MS. Butyryl-L-carnitine is a butyrate ester of carnitine. It is an inhibitor of intestinal transporters, blocking carnitine uptake by the carnitine transporter and glycine transport by the amino acid transporter in human retinal pigment epithelial (HRPE) cells (IC50s = 1.5 μM and 4.6 mM, respectively).
(R)-Butyryl Carnitine-d3 Chloride, is a labeled analogue of (R)-Butyryl Carnitine Chloride (B802700), a potential prodrug of Carnitine, used for treating seizure disorders.