Uses
2,3-Dihydroxyisovaleric acid (2,3-Dihydroxy-3-methylbutanoic acid) is a natural metabolite of the branched-chain amino acid leucine that has been found present in the urine of a patient with 2-hydroxyglutaric aciduria[1].
Definition
ChEBI: A dihydroxy monocarboxylic acid that is isovaleric acid which is substituted by hydroxy groups at positions 2 and 3.
References
[1] F B Armstrong, et al. Stereoselectivity and stereospecificity of the alpha,beta-dihydroxyacid dehydratase from Salmonella typhimurium. Biochim Biophys Acta. 1977 Jul 21;498(1):282-93. DOI:
10.1016/0304-4165(77)90266-5