Description
Isoleucine is a mixture of the diastereomers L-isoleucine, L-alloisoleucine, D-isoleucine, and D-alloisoleucine. L-Isoleucine is an essential branched-chain amino acid that acts as a nitrogen donor and has roles in glucose consumption, fatty acid metabolism, and immune function.1,2,3 L-Alloisoleucine is formed from L-isoleucine by transamination, and plasma levels of L-alloisoleucine are increased in patients with maple syrup urine disease (MSUD), an inborn error of metabolism characterized by branched-chain a-keto acid dehydrogenase (BCKAD) deficiency.4,5 D-Isoleucine and D-alloisoleucine are enantiomers of L-isoleucine and L-alloisoleucine, respectively. WARNING This product is not for human or veterinary use.
